PLA2R-positive (primary) membranous nephropathy in a child with IPEX syndrome.
Teresa ChuvaFrederick PfisterOrtraud BeringerKerstin FelgentreffMaike Büttner-HeroldKerstin AmannPublished in: Pediatric nephrology (Berlin, Germany) (2017)
This is the first report of a PLA2R-positive MN in a patient with IPEX syndrome. We suggest that, in this context, MN results from an autoimmune process against podocytic antigens, namely PLA2R.