Dental management of a 4-year-old child with congenital afibrinogenemia-A rare case report.
Shreya KhodkeIndu Miriam VarkeyKiran Dattatray GhuleShilpa S NaikAlthea DsouzaKajol ThakurShivani MehtaParnaja Sanjay ValkePublished in: Special care in dentistry : official publication of the American Association of Hospital Dentists, the Academy of Dentistry for the Handicapped, and the American Society for Geriatric Dentistry (2022)
Congenital afibrinogenemia is a rare hematologic disorder with an estimated incidence of 1-2 per million people worldwide. It is inherited as an autosomal recessive trait and is characterized by the inability to synthesize fibrinogen. Clinical features range from minimal bleeding to catastrophic hemorrhage. Because of its rarity, there are not enough clinical guidelines in the management of oral manifestations of patients with this disorder. The following case report presents the dental management of a 4-year-old child with congenital afibrinogenemia under general anesthesia. A multidisciplinary team approach was followed to achieve full mouth rehabilitation, thus improving the overall quality of life of the patient.