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Pigmented dermatofibrosarcoma (Bednar tumour) of scalp.

Apoorva AgarwalChanchal Rana
Published in: BMJ case reports (2023)
Pigmented dermatofibrosarcoma protuberans (DFSP) also known as Bednar tumour is a very rare variant of DFSP which is considered to be of intermediate grade along with the presence of melanin-containing dendritic cells. Only a handful of cases have been described in the literature so far. It is centred around the dermis or subcutis and can pose a diagnostic challenge by being confused with other pigmented lesions of the skin. We hereby report one such unusual case of a man in his late 20s presenting with swelling over the forehead for the past 7 years. Hence a diagnosis of pigmented DFSP should always be considered while reporting pigmented subcutaneous lesions with spindle cell morphology.
Keyphrases
  • dendritic cells
  • basal cell carcinoma
  • systematic review
  • immune response
  • single cell
  • emergency department
  • mesenchymal stem cells
  • regulatory t cells
  • soft tissue
  • adverse drug