Development of hepatic fibrosis in common variable immunodeficiency-related porto-sinusoidal vascular disorder.
Julian HercunBilal AsifAnusha VittalAbdel AhmedHarish Kumar Gopalakrishna PillaiJenna R E BergersonSteven HollandGulbu UzelWarren StroberIvan J FussChristopher KohDavid E KleinerTheo HellerPublished in: Alimentary pharmacology & therapeutics (2024)
In this CVID cohort, NRH is the most common initial histological finding; however, unexpectedly fibrosis progresses over time in a subgroup of patients. A better understanding of the underlying causal process of liver disease CVID might lead to improved outcomes.