Wild-type Cu/Zn-superoxide dismutase is misfolded in cerebrospinal fluid of sporadic amyotrophic lateral sclerosis.
Eiichi TokudaYo-Ichi TakeiShinji OharaNoriko FujiwaraIsao HozumiYoshiaki FurukawaPublished in: Molecular neurodegeneration (2019)
Taken together, we propose that misfolding of wild-type SOD1 in CSF is a common pathological process of ALS cases regardless of SOD1 mutations.