Severity scoring system to guide transfusion management in pediatric non-deletional HbH.
Duantida SongdejManunya TandhansakulPakawan WongwerawattanakoonNongnuch SirachainanPimlak CharoenkwanAmpaiwan ChuansumritPublished in: Pediatrics international : official journal of the Japan Pediatric Society (2023)
The newly developed scoring system was practical and helpful to highlight severely affected pediatric non-deletional HbH patients with potential needs of regular transfusion. This can be used as a guide for optimal treatment and disease monitoring in the future.