ISTH guidelines for the diagnosis of thrombotic thrombocytopenic purpura.
X Long ZhengSara K VeselySpero R CatalandPaul CoppoBrian GeldzilerAlfonso IorioMasanori MatsumotoReem A MustafaMenaka PaiGail RockLene RussellRawan TarawnehJulie ValdesFlora PeyvandiPublished in: Journal of thrombosis and haemostasis : JTH (2020)
There is a lack of high-quality evidence to support strong recommendations for the initial diagnosis and management of a suspected TTP. The panel emphasized the importance of obtaining ADAMTS13 testing in a proper clinical context. Future research should focus on how to monitor and act on ADAMTS13 levels during remission.