Eosinophilic granulomatosis with polyangiitis in children: Data from the French RespiRare® cohort.

Agnès FinaJean-Christophe DubusAntoine TranJocelyne DerellePhilippe ReixMichael FayonLaure CoudercMarie-Dominique DonnouAnne PagnierSylvain BlanchonNathalie FaureLaurent MelyMarc AlbertiniJacques de BlicLisa Giovannin-Chami

Published in: Pediatric pulmonology (2018)

This French cohort is the biggest pediatric EGPA series described to date, with a long follow-up period. The findings confirm that pediatric EGPA has specific clinical, radiological, and histological characteristics that differ from adult EGPA. Development of systemic symptoms, and consequently diagnosis, occur with a shorter delay in children, mainly during the eosinophilic phase and leading to a specific presentation.

Keyphrases

young adults
childhood cancer
chronic rhinosinusitis
big data
machine learning
physical activity
data analysis