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Incidence of thrombotic microangiopathies in Quebec: insight from a laboratory centralizing ADAMTS-13 testing.

Clémence MerlenEmmanuelle PépinOusmane BarryAnik CormierCaroline DuboisAnne-Laure LapeyraqueStéphan TroyanovGeorges-Etienne RivardArnaud Bonnefoy
Published in: Orphanet journal of rare diseases (2022)
The analysis of centralized data measuring ADAMTS-13 activity allowed us to adequately establish the incidence rate and demographic characteristics of TMA, particularly TTP, in Quebec. TTP incidence remained stable while suspected non-TTP TMA steadily increased from 2012 to 2019.
Keyphrases
  • risk factors
  • pulmonary embolism
  • big data