Spontaneous pseudoaneurysm of the aortic arch is an exceptionally rare and potentially life-threatening condition. In this case, we used contrast-enhanced echocardiography to demonstrate the diagnosis and recurrence of a 47-year-old female of aortic arch pseudoaneurysm. The use of contrast-enhanced echocardiography is suggested to be an important tool in the rapid diagnosis and postoperative follow-up of the aortic arch pseudoaneurysms.