Right ventricular epicardial arrhythmogenic substrate in long-QT syndrome patients at risk of sudden death.

Carlo Pappone Giuseppe Ciconte Luigi Anastasia Fiorenzo Gaita Edward R Grant Emanuele Micaglio Emanuela T Locati Žarko ĆalovićGabriele VicedominiVincenzo Santinelli

Published in: Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology (2023)

This study reveals that, among high-risk LQTS patients, regions localized in the epicardium of the right ventricle harbour structural electrophysiological abnormalities. Elimination of these abnormal electrical activities successfully prevented malignant ventricular arrhythmia recurrences.

Keyphrases

end stage renal disease
ejection fraction
newly diagnosed
chronic kidney disease
heart failure
peritoneal dialysis
left ventricular
pulmonary hypertension
pulmonary artery
pulmonary arterial hypertension