Spontaneous pneumothorax in a patient with multiple pulmonary arteriovenous malformations caused by hereditary hemorrhagic telangiectasia: a case report.
Yoshiaki TakaseHiroyoshi TsubochiSachiko NakanoTsukasa SuzukiToshiteru NagashimaOsamu KawashimaPublished in: Journal of surgical case reports (2020)
Spontaneous pneumothorax occurring in patients with pulmonary arteriovenous malformations (PAVMs) caused by hereditary hemorrhagic telangiectasia (HHT) is extremely rare. We report a case of spontaneous pneumothorax in a PAVM patient. A 26-year-old man with previously diagnosed HHT and multiple small PAVMs presented with chest pain and dyspnea and was referred to our hospital. Chest X-ray showed a left-sided pneumothorax. Computed tomography (CT) showed apical bullae on both sides of the upper lobe. We clarified the location of PAVMs by 3D-CT to avoid the massive bleeding caused by careless grasping of PAVMs and unintentional incomplete resection of the PAVMs during the pneumothorax surgery. Considering the risk of exacerbation, the patient underwent bullectomy of the left upper lobe. The postoperative histopathological examination indicated that the pneumothorax occurred spontaneously in the HHT patient. We should clarify the location of PAVMs to avoid bleeding caused by the grasping of PAVMs during surgery.
Keyphrases
- computed tomography
- case report
- dual energy
- minimally invasive
- pulmonary hypertension
- magnetic resonance imaging
- positron emission tomography
- atrial fibrillation
- image quality
- chronic obstructive pulmonary disease
- coronary artery bypass
- emergency department
- coronary artery disease
- extracorporeal membrane oxygenation
- mass spectrometry
- acute care
- drug induced
- mechanical ventilation