Acute Type A Dissection during Pregnancy with Marfan's Syndrome.
Christian HeimPhilipp P MüllerMichael WeyandFrank HarigPublished in: The Thoracic and cardiovascular surgeon reports (2021)
Background Marfan's syndrome (MFS) is a connective tissue disorder, caused by a mutation in the FBN-1 gene and affecting multiple organ systems including the vascular system. During pregnancy, women with MFS have an increased risk of aortic dissection due to changes in the cardiovascular system. Case Description We present a 39-year-old woman that suffered from an acute aortic dissection in week 33 of her third pregnancy who urgently required lifesaving surgery. Three-dimensional reconstruction of computed tomography scan was performed with unborn child in utero. Conclusion Monitoring of patients with suspected or confirmed MFS appears essential and interdisciplinary treatment and prevention strategies are required.
Keyphrases
- aortic dissection
- computed tomography
- case report
- positron emission tomography
- mental health
- magnetic resonance imaging
- coronary artery bypass
- genome wide
- copy number
- clinical trial
- atrial fibrillation
- dual energy
- magnetic resonance
- dna methylation
- coronary artery disease
- pregnancy outcomes
- drug induced
- pet ct
- aortic aneurysm