Login / Signup

Endovascular closure of a congenital extrahepatic portosystemic shunt for the treatment of hepatopulmonary syndrome in an infant.

Sai BhatteAnne Marie CahillMichelle DunnAnn ForanAdriana PerezMichael R Acord
Published in: Pediatric radiology (2023)
Congenital portosystemic shunts may result in the development of hepatopulmonary syndrome, typically presenting with progressive hypoxemia in later childhood. We describe a case of a 5-month-old male with heterotaxy with polysplenia presenting with new onset hypoxemia. Subsequent evaluation identified an extrahepatic portosystemic shunt arising from the confluence of the main portal and superior mesenteric veins draining into the left renal vein. To treat his hypoxemia and prevent future complications of shunting, the patient underwent a successful single-stage endovascular closure.
Keyphrases
  • case report
  • pulmonary artery
  • multiple sclerosis
  • risk factors
  • aortic dissection
  • coronary artery
  • early life
  • smoking cessation
  • clinical evaluation