The French paediatric cohort of Castleman disease: a retrospective report of 23 patients.

Charlotte BoroccoClaire Ballot-SchmitOanez AckermannNathalie AladjidiJeremie DelaleuVannina Giacobbi-MiletSarah JannierEric JeziorskiFrançois MaurierYves PerelChristophe PiguetEric OksenhendlerIsabelle Koné-PautCaroline Galeotti

Published in: Orphanet journal of rare diseases (2020)

Paediatric CD still seems underdiagnosed, with a significant diagnosis delay, especially for MCD, but new international criteria will help in the future. Unlike adult CD, which is strongly associated with HIV and human herpesvirus 8 infection, paediatric CD could be favored by primary activation of innate immunity and may affect life expectancy less.

Keyphrases

intensive care unit
emergency department
end stage renal disease
endothelial cells
chronic kidney disease
newly diagnosed
ejection fraction
nk cells
hiv infected
antiretroviral therapy
prognostic factors
hepatitis c virus
hiv aids
young adults
south africa