Comparison between idiopathic and VEXAS-relapsing polychondritis: analysis of a French case series of 95 patients.
Mohamed-Yacine KhitriAlexis F GuédonStéphanie Ducharme-BénardBenjamin TerrierDavid SaadounJulie SeguierMaelle le BesneraisClaire De MoreuilGuillaume DenisMathieu Gerfaud-ValentinJean Sebastien AllainAlexandre MariaLaurence BouilletVincent GrobostJoris GallandOlivier KosmiderAnael DumontMathilde DevauxBenjamin SubranJean SchmidtPaola Marianetti-GuingelSylvain AudiaSylvain PalatMarielle Roux-SauvatVincent JachietPierre HirschOlivier FainArsenne Mekiniannull nullPublished in: RMD open (2022)
We report the largest cohort of VEXAS-RP, characterised by high prevalence of male sex, fever, skin lesion, ocular involvement, pulmonary infiltration, heart involvement, older age and MDS association.