Epidemiology of hereditary transthyretin amyloidosis in the northernmost region of Sweden: a retrospective cohort study.
Jorge Mejia BarandaJenny LjungbergJonas WixnerIntissar AnanViktor OskarssonPublished in: Amyloid : the international journal of experimental and clinical investigation : the official journal of the International Society of Amyloidosis (2022)
The incidence of ATTRv amyloidosis increased 3-fold in Norrbotten between 2006 and 2018, most likely due to a previous underdiagnosis - with suggestions of lowered mortality during later years, possibly due to the introduction of disease-modifying drugs.