External validation of the HCM Risk-Kids model for predicting sudden cardiac death in childhood hypertrophic cardiomyopathy.
Gabrielle NorrishChen QuElla FieldElena CerviDiala KhraicheSabine KlaassenTiina H OjalaGianfranco SinagraHirokuni YamazawaChiara MarroneAnca PopoiuFernando CentenoSylvie SchouveyIacopo OlivottoSharlene M DaySteve ColanJoseph RossanoSamuel G WittekindSara SaberiMark RussellAdam HelmsJodie InglesChristopher SemsarianPerry M ElliottCarolyn Y HoRumana Z OmarJuan P KaskiPublished in: European journal of preventive cardiology (2021)
This study reports the first external validation of the HCM Risk-Kids model in a large and geographically diverse patient population. A 5-year predicted risk of ≥6% identified over 70% of events, confirming that HCM Risk-Kids provides a method for individualized risk predictions and shared decision-making in children with HCM.