Clinical significance of family history and bicuspid aortic valve in children and young adult patients with Marfan syndrome.
Emanuele MondaAdelaide FuscoDaniela MelisMartina CaiazzaFelice GragnanoAlfredo MaurielloAnnapaola CirilloMarta RubinoAugusto EspositoAngelina GrammegnaStefano NistriGuglielmina PepePaolo CalabròPietro StrisciuglioAlessandro Della CorteGuido OppidoMariagiovanna RussoGiuseppe LimongelliPublished in: Cardiology in the young (2020)
In our cohort of patients with Marfan syndrome, the absence of family history and the presence of bicuspid aortic valve were associated to severe aortic phenotype and worse prognosis.