Delineating associations of progressive pleuroparenchymal fibroelastosis in patients with pulmonary fibrosis.
Eyjolfur GudmundssonAn ZhaoNesrin MogulkocFrouke van BeekTinne GoosChristopher J BreretonMarcel VeltkampRobert ChapmanHendrik W van EsHelen GarthwaiteBahareh GholipourMelissa HeightmanArjun NairKatarina PontoppidanRecep SavaşAsia AhmedMarie VermantOmer UnatAlex ProcterDe Sadeleer LaurensEmma K DennenyTimothy WallisMark DuncanMagali TaylorStijn VerledenSamuel M JanesDaniel C AlexanderAthol U WellsJoanna C PorterMark G JonesIain D StewartColine H M van MoorselWim A WuytsJoseph JacobPublished in: ERJ open research (2023)
Progression of PPFE-like lesions independently associates with mortality in IPF and FHP but does not associate strongly with measures of fibrosis progression.