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Ongoing retinal degeneration despite intraventricular enzyme replacement therapy with cerliponase alfa in late-infantile neuronal ceroid lipofuscinosis type 2 (CLN2 disease).

Simon DulzC SchweringJan WildnerChristoph SpartalisFrank SchuettaufUdo BartschEva WibbelerMiriam NickelMartin Stephan SpitzerYevgeniya AtiskovaAngela Schulz
Published in: The British journal of ophthalmology (2022)
NCT04613089.
Keyphrases
  • replacement therapy
  • smoking cessation
  • optical coherence tomography
  • diabetic retinopathy
  • optic nerve
  • cerebral ischemia