Estrogen Receptor α Inactivation in 2 Sisters: Different Phenotypic Severities for the Same Pathogenic Variant.
Clémence DelcourNahla KhawajaSergio Gonzalez-DuqueSophie LebonAbir TalbiLeila DriraDidier ChevenneKamel M AjlouniNicolas de RouxPublished in: The Journal of clinical endocrinology and metabolism (2022)
These 2 new cases are remarkable given the difference in the severity of their ovarian and hormonal phenotypes. This phenotypic discrepancy may be due to a mechanism partially compensating for the ERα loss of function.