Charcot-Marie-Tooth Disease and Hearing Loss: A Systematic Review With Meta-Analysis.
John F MillsLuke D HeilandShaun A NguyenMichaela F CloseTed A MeyerPublished in: Otology & neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology (2024)
Patients with CMT can present with a variety of phenotypes depending on the causative mutation. The ABR interpeak latency values for the most common demyelinating form of CMT are delayed when compared to matched controls. Most subtypes have normal hearing thresholds, apart from CMT4C, which presents with mild hearing loss on average.
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