Clinical differences among patients with myeloperoxidase-antineutrophil cytoplasmic antibody-positive interstitial lung disease.

Koichi Yamaguchi Aya Yamaguchi Masashi ItoIkuo WakamatsuMiki Itai Sohei Muto Shogo Uno Masaki Aikawa Shunichi Kouno Masao Takemura Masakiyo Yatomi Haruka Aoki-Saito Yasuhiko Koga Kenichiro Hara Shinsuke Motegi Mayuko Tsukida Fumie Ota Yoshito Tsukada Mitsuru Motegi Masao Nakasatomi Toru Sakairi Hidekazu Ikeuchi Yoriaki Kaneko Keiju Hiromura Toshitaka Maeno

Published in: Clinical rheumatology (2022)

The subtypes of MPO-ANCA-positive ILD have different clinical features and prognoses. Patients who develop AE-ILD require careful evaluation of clinical courses. Key Points • In myeloperoxidase (MPO)-antineutrophil cytoplasmic antibody (ANCA)-positive interstitial lung disease (ILD), patients with unclassifiable vasculitis showed a better prognosis than those with idiopathic ILD.. • Development of acute exacerbation in ILD was a strong poor prognostic factor in patients with MPO-ANCA-positive ILD..

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