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Comparison of echocardiographic parameters in Fabry cardiomyopathy and light-chain cardiac amyloidosis.

Josef MarekTomas PalecekJulien MagneDavid LavergneCyrille BoulogneBahaa M FadelArnaud JaccardAles LinhartDania Mohty
Published in: Echocardiography (Mount Kisco, N.Y.) (2018)
Matched AL patients had worse LV diastolic function than FC, driven by E/e'. Significant LV systolic dysfunction was rare overall. MidFS and E/e' were associated with heart failure severity in both groups.
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