Spectrum and Prognosis of Antineutrophil Cytoplasmic Antibody-associated Vasculitis-related Bronchiectasis: Data from 61 Patients.
Raphael LhoteMarie ChillesMatthieu GrohXavier PuéchalPhilippe GuilpainFélix AckermannZahir AmouraIsabella Annesi-MaesanoThomas BarbaEmilie CatherinotFleur Cohen-AubartPascal CohenVincent CottinLouis-Jean CoudercHubert De BoyssonXavier DelbrelStéphane DominiquePierre DuhautOlivier FainEric HachullaMohamed HamidouJean-Emmanuel KahnChristophe LegendreAlain Le QuellecFrançois LhoteFrançois LifermannAlexis MathianAntoine NéelHilario NunesJean-François SubraBenjamin TerrierLuc MouthonElisabeth DiotLoïc GuillevinPierre-Yves BrilletColas Tcherakiannull nullPublished in: The Journal of rheumatology (2019)
The association of bronchiectasis with AAV is likely not accidental and is mostly associated with MPO-ANCA. Patients in whom bronchiectasis precedes the onset of AAV tend to have distinct clinical and biological features and could carry a worse prognosis.