Worldwide Incidence and Prevalence of Neuromyelitis Optica: A Systematic Review.
Viktoria PappMelinda MagyariOrhan AktasThomas BergerSimon A BroadleyPhilippe CabreAnu JacobJun-Ichi KiraMaria Isabel LeiteRomain MarignierKatsuichi MiyamotoJacqueline PalaceAlbert SaizMaria SepúlvedaOlafur SveinssonZsolt IllesPublished in: Neurology (2020)
NMOSD is a rare disease worldwide. Variations in prevalence and incidence have been described among different geographic areas and ethnicities. These are only partially explained by different study methods and NMO/NMOSD definitions, highlighting the need for specifically designed epidemiologic studies to identify genetic effects and etiologic factors.