Decreased outlet angle of the superior cerebellar artery as indicator for dolichoectasia in late onset Pompe disease.

Ole HenselIlka SchneiderMathias WieprechtTorsten KrayaStephan Zierz

Published in: Orphanet journal of rare diseases (2018)

Pompe disease is associated with BA dilation, elongation and elevated bifurcation height of the BA which might result in cerebrovascular complications. The SUCA outlet angle seems to be useful for monitoring the progression of BA dolichoectasia.

Keyphrases

late onset
early onset
high resolution
body mass index
risk factors
replacement therapy
cell wall