Clinical, tomographic and functional comparison of sporadic and tuberous sclerosis complex-associated forms of lymphangioleiomyomatosis: a retrospective cohort study.
Martina Rodrigues OliveiraMark WanderleyCarolina Salim Gonçalves FreitasRonaldo Adib KairallaRodrigo Caruso ChateAlexandre Franco AmaralFabio Eiji ArimuraLuciana Paula SamoranoElieser Hitoshi WatanabeCarlos Roberto Ribeiro CarvalhoBruno Guedes BaldiPublished in: ERJ open research (2024)
Greater functional decline and a higher cystic extension were found in patients with S-LAM. Our study provides a broad clinical, functional and tomographic characterisation of patients with LAM, adding valuable information to the existing evidence to better understand the two forms of the disease.