Arrhythmic risk prediction in arrhythmogenic right ventricular cardiomyopathy: external validation of the arrhythmogenic right ventricular cardiomyopathy risk calculator.
Paloma JordaLaurens P BosmanAlessio GasperettiAndrea MazzantiJean Baptiste GourraudBrianna DaviesTanja Charlotte FrederiksenZoraida Moreno WeidmannAndrea Di MarcoJason D RobertsCiorsti MacIntyreColette SeiferAntoine DelinièreWael AlqarawiDeni KukavicaDamien MinoisAlessandro TrancuccioMarine ArnaudMattia TargettiAnnamaria MartinoGiada OlivieroDaniel C PipilasCorrado CarbucicchioPaolo CompagnucciAntonio Dello RussoIacopo OlivottoLeonardo CalòSteven A LubitzMichael J CutlerPhilippe ChevalierElena ArbeloSilvia Giuliana PrioriJeffrey S HealeyHugh CalkinsMichela CasellaHenrik Kjærulf JensenClaudio TondoRafik TadrosCynthia A JamesAndrew D KrahnJulia Cadrin-TourignyPublished in: European heart journal (2022)
Using a large independent cohort of patients, this study shows that the ARVC risk model provides good prognostic information and outperforms other published decision algorithms for ICD use. These findings support the use of the model to facilitate shared decision making regarding ICD implantation in the primary prevention of SCD in ARVC.