Myocardial oedema in an 8-year-old Chinese boy with Idiopathic systemic capillary leak syndrome.
Karen Ka Yan LeungJaime Sou Rosa DuqueKwong-Man YuKai-Ning CheongPatrick Chun-Yin ChongMarco Hok-Kung HoPak-Cheong ChowPublished in: BMC pediatrics (2019)
ISCLS is rare, and therefore there is only a limited understanding on the pathophysiology of this disorder. The current treatment approach is based on a few case reports and series. During the acute phase, optimal supportive management is paramount. Our case highlights the importance of early recognition and consideration for extracorporeal membrane oxygenation support in patients with a life-threatening presentation, as it was lifesaving for this child who suffered myocardial oedema and ventricular dysfunction.