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Right ventricular epicardial arrhythmogenic substrate in long-QT syndrome patients at risk of sudden death.

Carlo PapponeGiuseppe CiconteLuigi AnastasiaFiorenzo GaitaEdward R GrantEmanuele MicaglioEmanuela T LocatiŽarko ĆalovićGabriele VicedominiVincenzo Santinelli
Published in: Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology (2023)
This study reveals that, among high-risk LQTS patients, regions localized in the epicardium of the right ventricle harbour structural electrophysiological abnormalities. Elimination of these abnormal electrical activities successfully prevented malignant ventricular arrhythmia recurrences.
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