Mounier-Kuhn syndrome: a case of tracheal smooth muscle remodeling.
Daniel P CookRyan J AdamMahmoud H Abou AlaiwaMichael EberleinJulia A Klesney-TaitKalpaj R ParekhDavid K MeyerholzDavid A StoltzPublished in: Clinical case reports (2016)
Mounier-Kuhn syndrome is a rare clinical disorder characterized by tracheobronchial dilation and recurrent lower respiratory tract infections. While the etiology of the disease remains unknown, histopathological analysis of Mounier-Kuhn airways demonstrates that the disease is, in part, characterized by cellular changes in airway smooth muscle.