10-year survival of pulmonary arterial hypertension associated with connective tissue disease: insights from a multicenter PAH registry.
Xiaoxi ChenRui-Lin QuanYuling QianZhenwen YangZaixin YuCaojin ZhangYuanhua YangGangcheng ZhangJieyan ShenQian WangQing GuChangming XiongXiaoli JingHuijun HanJian-Guo HePublished in: Rheumatology (Oxford, England) (2023)
The 10-year survival rate of CTD-PAH patients was reported for the first time. The 10-year prognosis was poor, but there was a tendency for more standardized treatment and better survival in patients enrolled after 2015. The recommended 4-strata model at follow-up can effectively predict 10-year survival in CTD-PAH patients.