Relationship between aetiology and left ventricular systolic dysfunction in hypertrophic cardiomyopathy.
Stefania RosminiElena BiaginiCostantinos O'MahonyHeerajnarain BulluckNiccolo' RuoziLuis R LopesOliver GuttmannPatricia ReantCristina C QuartaAntonis PantazisMaria Tome-EstebanWilliam J MckennaClaudio RapezziPerry Mark ElliottPublished in: Heart (British Cardiac Society) (2016)
In adults with HCM, LV systolic dysfunction is more frequent in those with rare phenocopies. When combined with age at presentation, it is a marker for specific aetiologies and is associated with poorer long-term survival.