Clinical Features, Genetic Findings, and Risk Stratification in Arrhythmogenic Right Ventricular Cardiomyopathy: Data From a Brazilian Cohort.
Natália Quintella Sangiorgi OlivettiLuciana SacilottoFanny WulkanGabrielle D'Arezzo PessenteMariana Lombardi Peres de CarvalhoDanilo Bora MoletaDenise Tessariol HachulPedro VeroneseCarina A HardyCristiano Faria PisaniTan Chen WuMarcelo Luiz Campos VieiraLucas Arraes de FrançaMatheus de Souza FreitasCarlos Eduardo RochitteSávia Christina BuenoVitor Bastos LovisiJose Eduardo KriegerMauricio Ibrahim ScanavaccaAlexandre da Costa PereiraFrancisco Carlos da Costa DarrieuxPublished in: Circulation. Arrhythmia and electrophysiology (2023)
Our study demonstrated the characteristics of a specific cohort with a high prevalence of arrhythmic burden at presentation, male predominance, younger age and HF severe outcomes. Our main results suggest that the presence and extension of low QRS voltage can be a risk predictor for HF-death/HTx in ARVC patients, regardless of the arrhythmic risk. This study can contribute to the global ARVC risk stratification, adding new insights to the international current scientific knowledge.