Cepacia syndrome in cystic fibrosis: a systematic review of the literature and possible new perspectives in treatment.

This study describes epidemiological, clinical characteristics and prognosis of CS cases reported over the last 24 years. CS is a rare yet severe complication of BCC infection in patients with CF, which occurs several years after BCC colonization and has a negative outcome in 50% of the patients. Data are too scanty to identify the most effective therapeutic approach. This article is protected by copyright. All rights reserved.