Cepacia syndrome in cystic fibrosis: A systematic review of the literature and possible new perspectives in treatment.
Valeria DaccòGianfranco AlicandroAlessandra ConsalesChiara RosazzaCalogero S SciarrabbaLisa CarianiCarla ColomboPublished in: Pediatric pulmonology (2023)
This study describes epidemiological, clinical characteristics, and prognosis of CS cases reported over the last 24 years. CS is a rare yet severe complication of BCC infection in patients with CF, which occurs several years after BCC colonization and has a negative outcome in 50% of the patients. Data are too scanty to identify the most effective therapeutic approach.
Keyphrases
- cystic fibrosis
- end stage renal disease
- newly diagnosed
- ejection fraction
- chronic kidney disease
- pseudomonas aeruginosa
- prognostic factors
- lung function
- early onset
- electronic health record
- machine learning
- patient reported outcomes
- chronic obstructive pulmonary disease
- combination therapy
- patient reported
- drug induced
- artificial intelligence
- replacement therapy
- smoking cessation