A case report of idiopathic pleuroparenchymal fibroelastosis with severe respiratory failure in pregnancy.
Aiko SekineKohei SeoSatoshi MatsukuraMasaaki SatoAya Shinozaki-UshikuTakashi OguraAkihiko KitamiMitsutaka KadokuraSatoshi DohiKiyotake IchizukaMasaaki NagatsukaPublished in: BMC pulmonary medicine (2020)
Our experience suggested that when pregnancy is complicated by PPFE, the disease may deteriorate rapidly. In this case, even though IPPFE with acute exacerbation was diagnosed during pregnancy, live birth was achieved, and the mother survived after lung transplantation. Lung transplantation should be considered in these patients because, once advanced, pulmonary lesions may be irreversible.
Keyphrases
- respiratory failure
- extracorporeal membrane oxygenation
- acute respiratory distress syndrome
- mechanical ventilation
- end stage renal disease
- preterm birth
- pregnancy outcomes
- ejection fraction
- chronic obstructive pulmonary disease
- newly diagnosed
- pulmonary hypertension
- liver failure
- prognostic factors
- drug induced
- early onset
- patient reported