Comparative analysis of right ventricular strain in Fabry cardiomyopathy and sarcomeric hypertrophic cardiomyopathy.
Maria Chiara MeucciRosa LilloAntonella LombardoGaetano A LanzaMarianne BootsmaSteele C ButcherMassimo MassettiRaffaele MannaJeroen J BaxThomas F LüscherNina Ajmone MarsanFrancesco MarianiPublished in: European heart journal. Cardiovascular Imaging (2022)
Patients with FC show a specific pattern of RV myocardial mechanics, characterized by a larger impairment of RV-FWS and lower ΔRV strain in comparison to patients with HCM, which may be helpful in the differential diagnosis between these two diseases.