An infant with LUMBAR syndrome complicated by severe perineal ulceration managed with diverting colostomy.
Malgorzata K NowakowskaEdgar D RodriguezRaegan D HuntKristy L RialonSiddharth P JadhavDenise W MetryPublished in: Pediatric dermatology (2022)
Infantile hemangiomas are the most common childhood vascular lesions. LUMBAR syndrome (lower body hemangioma, urogenital abnormalities/ulceration, myelopathy, bony deformities, anorectal malformations/arterial anomalies, and rectal anomalies) warrants special treatment considerations. Here we describe a case of an infant with LUMBAR syndrome who presented with severe perineal ulceration refractory to standard medical therapy and was managed with a temporary diverting sigmoid colostomy. This case demonstrates that adjunctive surgical management can be considered in infants with aggressive perineal wounds refractory to standard medical therapy.