Intracranial Arterial Tortuosity in Marfan Syndrome and Loeys-Dietz Syndrome: Tortuosity Index Evaluation Is Useful in the Differential Diagnosis.
Luca SpinardiGianfranco VornettiSara Rosa Maria De MartinoRita GolfieriL FaccioliM Pastore TrosselloClaudio GrazianoMaria Elisabetta MariucciAndrea DontiPublished in: AJNR. American journal of neuroradiology (2020)
The tortuosity index of intracranial arteries is an easily calculated and highly reproducible measure, which shows a high specificity for Marfan syndrome and Loeys-Dietz syndrome and may be useful in differentiating these 2 entities.