Contemporary Management of the Failing Fontan.
Prashanth VenkateshHans GaoIslam AbudayyehRamdas G PaiPadmini VaradarajanPublished in: Journal of clinical medicine (2024)
Adult patients with congenital heart disease have now surpassed the pediatric population due to advances in surgery and improved survival. One such complex congenital heart disease seen in adult patients is the Fontan circulation. These patients have complex physiology and are at risk for several complications, including thrombosis of the Fontan pathway, pulmonary vascular disease, heart failure, atrial arrhythmias, atrioventricular valve regurgitation, and protein-losing enteropathy. This review discusses the commonly encountered phenotypes of Fontan circulatory failure and their contemporary management.
Keyphrases
- congenital heart disease
- heart failure
- end stage renal disease
- ejection fraction
- aortic valve
- aortic stenosis
- newly diagnosed
- minimally invasive
- chronic kidney disease
- atrial fibrillation
- pulmonary hypertension
- mitral valve
- peritoneal dialysis
- pulmonary embolism
- prognostic factors
- left ventricular
- risk factors
- catheter ablation
- coronary artery disease
- transcatheter aortic valve replacement
- amino acid
- small molecule
- left atrial
- surgical site infection