Significance of PR3-ANCA positivity in eosinophilic granulomatosis with polyangiitis (Churg-Strauss).
Matthias PapoRenato A SinicoVítor TeixeiraNils VenhoffMaria-Letizia UrbanMichele IudiciJuliane MahrholdFrancesco LocatelliGiulia CassoneFranco SchiavonBenjamin SeeligerThomas NeumannClaus KroegelMatthieu GrohChiara MarvisiMaxime SamsonThomas BarbaDavid JayneArianna TroiloJens ThielBernhard HellmichSara MontiCarlomaurizio MontecuccoCarlo SalvaraniJean-Emmanuel KahnBernard BonnotteCécile-Audrey DurelXavier PuéchalLuc MouthonLoïc GuillevinGiacomo EmmiAugusto VaglioBenjamin Terriernull nullPublished in: Rheumatology (Oxford, England) (2021)
PR3-ANCA EGPA patients differ from those with MPO-ANCA and negative ANCA, and share clinical features with granulomatosis with polyangiitis. This suggests that PR3-ANCA EGPA could be a particular form of PR3-ANCA-associated vasculitis.