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RNF170-Related Hereditary Spastic Paraplegia: Confirmation by a Novel Mutation.

Jean-Madeleine de Sainte AgatheSandra MercierJean-Yves MahéYann PéréonJulien BurattiLaurène TissierBophara KolSamia Ait SaidÉric LeguernGuillaume BanneauGiovanni Stévanin
Published in: Movement disorders : official journal of the Movement Disorder Society (2020)
We confirm the involvement of biallelic truncating variants in RNF170 in a novel form of hereditary spastic paraplegia. © 2020 International Parkinson and Movement Disorder Society.
Keyphrases
  • cerebral palsy
  • botulinum toxin
  • upper limb
  • dna damage response
  • copy number
  • oxidative stress
  • autism spectrum disorder
  • dna damage
  • drug induced