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Paediatric sickle cell disease at a tertiary hospital in Malawi: a retrospective cross-sectional study.

Chikondi Sharon ChimbatataMaster R O ChisaleAlfred Bornwell KayiraFrank Watson SinyizaBalwani Chingatichifwe MbakayaPaul Uchizi KasekaPocha KamudumuliTsung-Shu Joseph Wu
Published in: BMJ paediatrics open (2021)
Anaemia, sepsis and painful crisis were the most common clinical features paediatric patients with SCD presented with. Patients with painful crisis were more likely to have prolonged hospital stay. Delayed diagnosis of SCD is a problem that needs immediate attention in this setting. Although somewhat encouraging, the relatively low in-hospital mortality among SCD children may under-report the true mortality from the disease considering community deaths and deaths occurring before SCD diagnosis is made.
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