Characterisation of Pediatric Pulmonary Hypertensive Vascular Disease from the PPHNet Registry.
Steven H AbmanMary P MullenLynn A SleeperEric D AustinErika B RosenzweigJohn P KinsellaDunbar IvyRachel K HopperJ Usha RajJeffrey FinemanRoberta L KellerAngela BatesUsha S KrishnanCatherine M AvitabileAlexander DavidsonMarc D NatterKenneth D Mandlnull nullPublished in: The European respiratory journal (2021)
We find a striking proportion of pediatric PH patients with Group 3 disorders, reflecting the growing recognition of PH in diverse developmental lung diseases. Greater precision of clinical phenotyping based on disease-specific characterization may further enhance care and research of pediatric PH.