Experience of kidney transplantation to a patient with Bernard Soulier syndrome: A case report.
Cihan KarataşBaşak AkyolluEmre ArpaliBerna YelkenAydın TurkmenBurak KoçakPublished in: Turkish journal of surgery (2023)
Renal transplantation could be a challenging operation in patients with haemorrhagic diathesis, with predictable difficulties or even with unpredictable hurdles. Bernard Soulier Syndrome (BSS) is one of the ethiologies of the thrombocytopenia and it is a rare hereditary disease associated with defects of the platelet glycoprotein complex glycoprotein Ib/V/IX and characterized by large platelets, thrombocytopenia, and severe bleeding symptoms. Here, we present a challenging renal transplantation in BSS.