Progressive Early Interstitial Lung Abnormalities in Persons At-Risk for Familial Pulmonary Fibrosis: A Prospective Cohort Study.
Margaret L SalisburyCheryl MarkinTisra FadelyAdam R GuttentagStephen M HumphriesDavid A LynchJonathan A KropskiTimothy S BlackwellPublished in: American journal of respiratory and critical care medicine (2024)
In persons at-risk for FPF, minor interstitial abnormalities, including reticulation that is unilateral or involves <5% of a lung zone, frequently represent subclinical disease.