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Progressive Early Interstitial Lung Abnormalities in Persons At-Risk for Familial Pulmonary Fibrosis: A Prospective Cohort Study.

Margaret L SalisburyCheryl MarkinTisra FadelyAdam R GuttentagStephen M HumphriesDavid A LynchJonathan A KropskiTimothy S Blackwell
Published in: American journal of respiratory and critical care medicine (2024)
In persons at-risk for FPF, minor interstitial abnormalities, including reticulation that is unilateral or involves <5% of a lung zone, frequently represent subclinical disease.
Keyphrases
  • pulmonary fibrosis
  • multiple sclerosis
  • early onset