Impact of Elexacaftor/Tezacaftor/Ivacaftor Therapy on Lung Clearance Index and Magnetic Resonance Imaging in Children with Cystic Fibrosis and One or Two F508del Alleles.
Mirjam StahlMartha DohnaSimon Y GraeberOlaf SommerburgDiane M RenzSophia T PallenbergAndreas VoskrebenzevKatharina SchützGesine HansenFelix DoellingerEva SteinkeStephanie TheeJobst F RoehmelSandra BarthClaudia Rückes-NilgesJulian BergesSusanne HämmerlingMark Oliver WielpützLutz NaehrlichJens Vogel-ClaussenBurkhard TümmlerMarcus Alexander MallAnna-Maria DittrichPublished in: The European respiratory journal (2024)
alleles in a real-world setting. Our results support early initiation of ETI to reduce or even prevent lung disease progression in school-age children with CF.
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